endosergЭндокринная хирургияEndocrine Surgery2306-35132310-3965Типография «Печатных дел Мастер»10.14341/serg201414-26endoserg-6641Research ArticleСтатьиArticlesПроект российских клинических рекомендаций по диагностике и лечению адренокортикального ракаDraft of Russian Guidelines of Diagnosis and Treatment of Adrenal Cortical CancerMelnichenkoG A

Endocrinology Research Centre, Moscow, Russian Federation

-StilidiI S

N.N. Blokhin Russian Cancer Research Center, Moscow, Russian Federation

-GorbunovaV A

N.N. Blokhin Russian Cancer Research Center, Moscow, Russian Federation

-AlexeevB Ya

P.A. Hertsen Moscow Cancer Research Institute, Moscow, Russian Federation

-BeltsevichD G

Endocrinology Research Centre, Moscow, Russian Federation

beltsevich@rambler.ruRaykhmanA O

Sechenov First Moscow State Medical Univesity, Moscow, Russian Federation

-KuznetsovN S

Endocrinology Research Centre, Moscow, Russian Federation

-ZhukovN V

P.A. Hertsen Moscow Cancer Research Institute, Moscow, Russian Federation; Federal Scientific Clinical Centre of Pediatric Hematology Oncology Immunology named after Dvitry Rogachev, Moscow, Russian Federation

-BokhyanV Yu

N.N. Blokhin Russian Cancer Research Center, Moscow, Russian Federation

-20141503201481№1 (2014)426Copyright © Melnichenko G.A., Stilidi I.S., Gorbunova V.A., Alexeev B.Y., Beltsevich D.G., Raykhman A.O., Kuznetsov N.S., Zhukov N.V., Bokhyan V.Y., 20142014Melnichenko G.A., Stilidi I.S., Gorbunova V.A., Alexeev B.Y., Beltsevich D.G., Raykhman A.O., Kuznetsov N.S., Zhukov N.V., Bokhyan V.Y.Melnichenko G.A., Stilidi I.S., Gorbunova V.A., Alexeev B.Y., Beltsevich D.G., Raykhman A.O., Kuznetsov N.S., Zhukov N.V., Bokhyan V.Y.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.surg-endojournals.ru/jour/article/view/6641

Определение гормональной активности и злокачественного потенциала - актуальнейший вопрос диагностики и выбора лечебной тактики при опухолях надпочечников. Адренокортикальный рак (АКР) - достаточно редкое заболевание, которое характеризуется плохими прогностическими показателями. Встречаемость АКР - 0,5-2 случая на миллион населения, в структуре инциденталом надпочечников - не более чем 2-4% наблюдений. Для широкого обсуждения предлагается проект клинических рекомендаций по диагностике и лечению АКР, предназначенных для онкологов, хирургов, эндокринологов, специалистов по лучевой диагностике, патоморфологов и др.

Statement of hormonal activity and potential malignancy are the most important issues of diagnosis and selection of appropriate treatment way for patients with adrenal tumors. Adrenal cortical carcinoma (ACC) is rare disease with poor prognosis. Incidience of ACC is about 0.5-2 per million, and no more then 2-4% among adrenal tumors. This draft of guidelines of diagnosis and treatment of ACC is offered to common discussion among wide round of specialists.

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The authors declare that there are no conflicts of interest present.