endosergЭндокринная хирургияEndocrine Surgery2306-35132310-3965Типография «Печатных дел Мастер»10.14341/serg2014220-26endoserg-6760Research ArticleСтатьиArticlesКлинический случай адренокортикального рака при синдроме Беквита-ВидеманаA Late Onset of Adrenocortical Cancer Assosiated with Beckwith-Wiedemann SyndromeKuznetsovN S

Endocrinology Research Centre

-LatkinaN V

Endocrinology Research Centre

-KalinchenkoN Yu

Endocrinology Research Centre

-SelivanovaL S

Endocrinology Research Centre

-RaykhmanA O

I.M. Sechenov First Moscow State Medical University

toda_mi_alma@inbox.ru20141506201482№2 (2014)2026Copyright © Kuznetsov N.S., Latkina N.V., Kalinchenko N.Y., Selivanova L.S., Raykhman A.O., 20142014Kuznetsov N.S., Latkina N.V., Kalinchenko N.Y., Selivanova L.S., Raykhman A.O.Kuznetsov N.S., Latkina N.V., Kalinchenko N.Y., Selivanova L.S., Raykhman A.O.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://www.surg-endojournals.ru/jour/article/view/6760

Синдром Беквита-Видемана - это генетически обусловленное нарушение роста и развития с высоким риском канцерогенеза в детском возрасте. При синдроме Беквита-Видемана часто отмечают макроглоссию, грыжи передней брюшной стенки и макросомию. Первые восемь лет жизни особенно опасны в отношении развития неоплазии. Тем не менее данное клиническое наблюдение демонстрирует возможность поздней манифестации адренокортикального рака у пациентки с синдромом Беквита-Видемана.

Beckwith-Wiedemann syndrome (BWS) is a genetic overgrowth disorder involving a predisposition to tumor development. The common features of Beckwith-Wiedemann syndrome include omphalocele, macroglos- sia and macrosomia. The increased risk for neoplasia is concentrated in the first eight years of life. However, this case presents a late onset of adrenocortical cancer assosiated with Beckwith-Wiedemann syndrome.

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The authors declare that there are no conflicts of interest present.