A Late Onset of Adrenocortical Cancer Assosiated with Beckwith-Wiedemann Syndrome
https://doi.org/10.14341/serg2014220-26
Abstract
Beckwith-Wiedemann syndrome (BWS) is a genetic overgrowth disorder involving a predisposition to tumor development. The common features of Beckwith-Wiedemann syndrome include omphalocele, macroglos- sia and macrosomia. The increased risk for neoplasia is concentrated in the first eight years of life. However, this case presents a late onset of adrenocortical cancer assosiated with Beckwith-Wiedemann syndrome.
About the Authors
N S KuznetsovEndocrinology Research Centre
N V Latkina
Endocrinology Research Centre
N Yu Kalinchenko
Endocrinology Research Centre
L S Selivanova
Endocrinology Research Centre
A O Raykhman
I.M. Sechenov First Moscow State Medical University
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Review
For citations:
Kuznetsov N.S., Latkina N.V., Kalinchenko N.Yu., Selivanova L.S., Raykhman A.O. A Late Onset of Adrenocortical Cancer Assosiated with Beckwith-Wiedemann Syndrome. Endocrine Surgery. 2014;8(2):20-26. (In Russ.) https://doi.org/10.14341/serg2014220-26
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